Japanese Journal of Cardiovascular Surgery Vol46,No4

Aortic Arch Aneurysm 7 Years after Aortic Root Replacement in a Patient of Loeys-Dietz Syndrome

Jun Hayashi* Seigo Gomi* Tetsuro Uchida*
Azumi Hamasaki* Yoshinori Kuroda* Atsushi Yamashita*
Ken Nakamura* Daisuke Watanabe* Shingo Nakai*
Akihiro Kobayashi* Mitsuaki Sadahiro*

(Second Department of Surgery, Yamagata University Faculty of Medicine*, Yamagata, Japan)

A 14-year-old women who had a history of aortic root replacement at 7 years old admitted our hospital due to dilatation of aortic arch aneurysm. Loeys-Dietz syndrome was diagnosed when she was 10 years old. Computed tomography showed 70 mm proximal arch aneurysm. Operative findings revealed brachiocephalic artery and left common carotid artery branched from aneurysm. Partial arch replacement was performed and distal anastomosis was made between left common carotid artery and left subclavian artery. Close observation by CT regularly is necessary and undergo aortic repair not to miss the timing of surgery. 

Jpn. J. Cardiovasc. Surg. 46:157-160(2017)

Keywords:Loeys-Dietz syndrome;Marfan syndrome;aortic aneurysm;reoperation

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